Purpose
To describe a central retinal artery occlusion in a patient with antineutrophil cytoplasmic antibody (ANCA) negative Churg-Strauss
syndrome.
Methods
Review of clinical and laboratory findings of a 44-year-old woman with ANCA negative Churg-Strauss syndrome that developed
sudden vision loss in left eye.
Results
Left central retinal artery occlusion was diagnosed by retinal whitening, a cherry-red spot, and delayed arterial filling
on fluorescein angiography. Perinuclear ANCA and cytoplasmic ANCA were negative.
Conclusion
Central retinal artery occlusion can occur in ANCA negative Churg-Strauss syndrome. Patients with this diagnosis should be
considered for prophylactic high dose corticosteroid, regardless of their ANCA status.
Keywords ANCA - Central retinal artery occlusion - Churg-Strauss syndrome