Different types of migraine have been reported in 20–40% of patients with cerebral autosomal dominant arteriopathy with subcortical
infarcts and leukoencephalopathy (CADASIL). We describe a novel migrainous manifestation of CADASIL consisting in status migrainosus
and persistent aura without infarction. The symptoms resolved after i.v. treatment with lorazepam and mannitol.
Keywords CADASIL - Migraine - Aura - Headache - Triptans - International Classification of Headache Disorders