These congenital, non-progressive lesions are benign, and often solitary and unilateral. Patients are usually asymptomatic, although some may experience decreased vision and neurologic symptoms, such as seizures and cranial nerve palsies [15, 87]. Cutaneous or cerebral hemangiomas may also be found, especially in cases of inherited lesions [2, 4, 15, 22, 23, 58]. Pedigree analysis suggests that this neurooculocutaneous syndrome may be inherited in an autosomal dominant pattern, with incomplete penetrance or variable expressivity [23, 58].